Treatment of Congenital Clubfoot in Freeman-Sheldon Syndrome Associated with Poland Syndrome. Case Report Masaki Nishiyama 1 , Kou Kato 2 , Masaya Tsujii 1 , Shigeto Nakazora 3 , Eiji Nii 1 1Department of Orthopaedic Surgery,Mie Prefectural Kusanomi Rehabilitation Center 2Department of Orthopaedic Surgery,Suzuka Kaisei General Hospital 3Department of Orthopaedic Surgery,School of Medicine,Mie University Keyword: Freeman-Sheldon syndrome(フリーマン・シェルドン症候群) , Poland syndrome(ポーランド症候群) , congenital clubfoot(先天性内反足) pp.93-97
Published Date 2005/1/1
DOI https://doi.org/10.11477/mf.1408100035
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We report a case of bilateral congenital clubfoot in Freeman-Sheldon syndome associated with Poland syndrome.

 A 4-year-old boy had a whistling-face and bilateral congenital clubfoot,which are common features of Freeman-Sheldon syndome,and also had absence of the right pectoralis muscles and hypoplasia and syndactyly of the right hand,which are characteristic of Poland syndome. Tenotomy of the Achilles tendon and posterior release were performed twice,once at 3months of age and again at 6months of age. But neither of these operations was sucessful. At a 2 years 8 months of age we performed bilateral posteromedial release,plantar fascia release,and abductor hallucis tendon release to achieve plantigrade feet,and at the most recent follow-up examination,at four years of age,there was no evidence of any tendency to recur. Congenital clubfoot in Freeman-Sheldon syndrome is difficult to treat,and wide soft tissue release is necessary to correct the deformity at the time of the initial surgery.

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