27歳発症進行性の運動失調，ミオクローヌス，痴呆を呈した60歳女性

A 60-year-old Woman with Progressive Cerebellar Ataxia, Myoclonus, and Dementia

症例呈示

　症例：S．T．，60歳，女性（93-76026）

　主訴：不随意運動，痴呆

We report a 60-year-old woman with progressive ataxia, myoclonus, choreoathetosis, and dementia. She was well until 27 years of the age when she noted an onset of gait disturbance and speech distur-bance. She noted abnormal involuntary movements in her four limbs at 42 years of the age. Her symp-toms had progressively become worse and she fell down frequently by her 52 years of the age. In addition, her family members noted gradual decline in her intelligence. She was admitted to our hospital in February of 1993 when she was 57-year-old.