先天性気管支閉鎖症と肺葉内肺分画症の同一肺葉内併存

Surgical Treatment for Congenital Bronchial Atresia and Intralobar Sequestration in the Same Lobe

先天性気管支閉鎖症は，胎生期に気管支が閉塞し，中枢側気管支との交通が絶たれ，末梢側気管支の拡張と末梢肺の過膨張をきたす疾患である．一方，肺葉内肺分画症は正常な気道系と交通がなく大循環系からの異常動脈によって灌流される肺組織を有する疾患である．われわれは，同一肺葉内に両症が併存した1例を経験したので報告する．

A 21-year-old man who had a history of pneumonia twice presented with chest discomfort. Computed tomography （CT） revealed dilatation of the atretic bronchus that was not continuous with the proximal one, and surrounding hyper-lucent lung fields in the outer and mediastinal sides of the right basal segment, and the absence of B10b＋c. CT also demonstrated the presence of A10b＋c in the former field and the aberrant artery from the inferior phrenic artery in the latter. Right basal segmentectomy was performed under the diagnosis of congenital bronchial atresia and intralobar sequestration. Pathological diagnosis accorded with preoperative one.